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Title: 偽性低アルドステロン症Ⅰ型を呈した両側原発性閉塞性巨大尿管症の1例
Other Titles: Pseudohypoaldosteronism Type 1 in an Infant with Bilateral Primary Obstructive Megaureter : A Case Report
Authors: 牧野, 雄樹  KAKEN_name
兼松, 明弘  KAKEN_name
今村, 正明  KAKEN_name
吉村, 耕治  KAKEN_name
西山, 博之  KAKEN_name
依藤, 亨  KAKEN_name
小川, 修  KAKEN_name
Author's alias: Makino, Yuki
Kanematsu, Akihiro
Imamura, Masaaki
Yoshimura, Koji
Nishiyama, Hiroyuki
Yorifuji, Tohru
Ogawa, Osamu
Keywords: Pseudohypoaldosteronism
Issue Date: Apr-2011
Publisher: 泌尿器科紀要刊行会
Journal title: 泌尿器科紀要
Volume: 57
Issue: 4
Start page: 193
End page: 197
Abstract: A 35-day-old male infant was referred to our hospital for bilateral hydroureteronephrosis on postnatal ultrasonography. He was born at 37 weeks and 2 days of gestation, weighing 2,765 g. He was diagnosed with bilateral primary obstructive megaureter. During observation, at 3 months and 2 weeks of age, he presented with dehydration and showed hyponatremia and hyperkalemia. An endocrinological examination led to a diagnosis of pseudohypoaldosteronism type 1 (PHA1). After bilateral percutaneous nephrostomy, PHA1 resolved. He underwent bilateral ureteral tapering and ureteroneocystostomy at 5 months and 3 weeks of age. Since PHA1 recurred after removal of urethral catheter, urethral catheter and bilateral double-J-stent was kept until 8 months old. He was followed-up until 3 years old with no signs of PHA1 recurrence. For an infant with obstructive uropathy or vesicoureteral reflux showing hyponatremia and hyperkalemia, PHA1 should be considered.
Rights: 許諾条件により本文は2012-05-01に公開
PubMed ID: 21646850
Appears in Collections:Vol.57 No.4

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