まれな合併症を伴ったFused Pelvic Kidneyの1例

Abstract

Fused pelvic kidney is very rare. Only five cases have previously been reported in Japan and less than twenty in the world. An 8-year-old boy was admitted to our hospital with chief complaint of gross hematuria of 3 days duration. Urological examination such as excretory urogram and abdominal aortography revealed a typical fused pelvic kidney with blood supply of one artery from the bifurcation of the aorta, Cystoscopic examination revealed a normotopic ureterocele on the left side. And other examinations revealed thoratic scoliosis and Recklinghausen's disease. Gross hematuria was considered due to hemorrhagic cystitis and he had no other lesion required any kinds of the treatment. Cases of the fused pelvic kidney in Japan were reviewed and terminology, embryology and complications of the fused pelvic kidney were discussed.