Persistent Mullerian Duct SyndromeにSeminomaを合併した1例

Abstract

Persistent Mullerian duct syndrome is a male hermaphroditism in which remnants of Mullerian ducts occur from abnormality of Mullerian inhibitory factor and often cause transverse testicular ectopia or hernia uteri inguinalis. A 22-year-old-man was admitted with the chief complaint of painless swelling of the right scrotal content. Preoperative diagnosis was right testicular tumor and left undescended testis. High orchiectomy was done. At operation left transverse testicular ectopia and a remnant Mullerian duct was found incidentally. The right testicular tumor was seminoma pT1. Sixty-seven cases of transverse testicular ectopia have been reported in Japan, 37 of which are reports of a remnant Mullerian duct. Ten of these cases were accompanied by tumors. The pathogenesis and treatment of persistent Mullerian duct syndrome were discussed with review of the literature.