腎被膜より発生したと思われる平滑筋芽細胞腫(Leiomyoblastoma)の1例

Abstract

A 45-year-old female visited our Department on February 7, 1986, with the principal complaint of swelling in the right upper abdomen. She was hospitalized on February 20. Ultrasonography, DIP, CT and right renal arteriography were performed. On March 10, the right kidney was extirpated transabdominally. The extirpated kidney weighed 1.2 kg and tightly adhered to the renal capsule. The kidney included a solid, yellowish white, homogeneous tumor. There was also a cyst outside of the tumor. The tumor was limited within, and easily separated from, Gerota's fascia. Pathological diagnosis revealed that the tumor was a leiomyoblastoma originated from the blood vessel. On March 26, postoperative VAC therapy (1 mg vincristine; 300 mg cyclophosphamide; 2 mg actinomycin D) was performed, and the patient was released from the hospital on April 8. As of August of 1987, no relapse of the disease has been detected. There have been very few reports of leiomyoblastoma in Japan. Whether leiomyoblastoma might take a malignant course was investigated to some extent on the basis of the reported literature.