膀胱外反症を伴ったPrune Belly Syndromeの1例

Abstract

A case of prune belly syndrome with an extrophy of the bladder was reported. A plasty of the bladder and a gastrostomy were done, but unfortunately, he died at age of 63 days. Autopsy revealed the absence of the abdominal musculature and some associated conditions, i.e. bilateral hydronephrosis, dilated ureters, bilateral cryptorchidism, phimosis, occlusio penis, congenital intestinal stenosis, pectus excavatum, persistent ostium secundum, abnormal lobation of the lungs, deformity of the liver and the spleen, the intramesenterial pancreas, malrotation of the gut with mesenterium commune, metatarsus varus and separation of pubic bone. To our knowledge, a case of an extrophy of the bladder in a prune belly syndrome was not reported in Japan.