このアイテムのアクセス数: 1166

このアイテムのファイル:
ファイル 記述 サイズフォーマット 
59_709.pdf867.19 kBAdobe PDF見る/開く
タイトル: 呼吸器症状を伴わずに偶発腫瘍として診断された後腹膜リンパ脈管筋腫症(LAM : lymphangiomyomatosis) の1例
その他のタイトル: A Case of Incidentally Diagnosed Retroperitoneal Lymphangioleiomyomatosis with No Respiratory Symptoms
著者: 田中, 建  KAKEN_name
宮崎, 淳  KAKEN_name
内田, 将央  KAKEN_name
市岡, 大士  KAKEN_name
木村, 友和  KAKEN_name
及川, 剛宏  KAKEN_name
末富, 崇弘  KAKEN_name
河合, 弘二  KAKEN_name
上杉, 憲子  KAKEN_name
那須, 克宏  KAKEN_name
西山, 博之  KAKEN_name
著者名の別形: Tanaka, Ken
Miyazaki, Jun
Uchida, Masahiro
Ichioka, Daishi
Kimura, Tomokazu
Oikawa, Takehiro
Suetomi, Takahiro
Kawai, Koji
Uesugi, Noriko
Nasu, Katsuhiro
Nishiyama, Hiroyuki
キーワード: Retroperitoneal mass
Lymphangiomyomatosis
発行日: Nov-2013
出版者: 泌尿器科紀要刊行会
誌名: 泌尿器科紀要
巻: 59
号: 11
開始ページ: 709
終了ページ: 713
抄録: A 39-year-old woman presented with a large retroperitoneal tumor found incidentally in a routine examination. The 138×37×26 mm mass was located in the left paraaortic region. Blood tests and urinalyses including endocrinological examinations revealed no abnormalities. A chest computed tomography revealed multiple thin-walled pulmonary cysts, which is a characteristic of lymphangioleiomyomatosis (LAM). Because the findings strongly suggested that the retroperitoneal tumor was an extrapulmonary manifestion of LAM, we performed laparoscopic resection of the tumor for diagnosis and treatment. The pathological diagnosis was LAM. The tumor cells were immunohistochemically positive for α -smooth muscle actin and weakly positive for HMB45, which is consistent with LAM. The cells were also positive for estrogen receptor (ER) and progesterone receptor (PgR). LAM is a rare progressive disease that affects mainly the lung, and leads to chronic respiratory failure. Extrapulmonary LAM without respiratory symptoms, is extremely rare. In the past, the prognosis of LAM was poor, with a median survival of 8-10 years, but now 85% survive more than 10 years. In the present case, deterioration of pulmonary lesions was not observed during the 10 months follow-up. Because ERand PgRfindings were positive, we will consider hormonal therapy as a treatment option, when the pulmonary lesions progress in the present case.
著作権等: 許諾条件により本文は2014-12-01に公開
URI: http://hdl.handle.net/2433/179612
PubMed ID: 24322407
出現コレクション:Vol.59 No.11

アイテムの詳細レコードを表示する

Export to RefWorks


出力フォーマット 


このリポジトリに保管されているアイテムはすべて著作権により保護されています。