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タイトル: | 腹腔内出血を契機として診断に至った結節性硬化症に合併した子宮Perivascular epithelioid cell tumor(PEComa)の1例 |
その他のタイトル: | A Case of Perivascular Epithelioid Cell Tumor (PEComa) of the Uterus Associated with Tuberous Sclerosis Complex Diagnosed by Intra-Abdominal Bleeding from the Uterus |
著者: | 谷口, 歩 角田, 洋一 藤田, 和利 植村, 元秀 木内, 寛 今村, 亮一 宮川, 康 野々村, 祝夫 上田, 豊 |
著者名の別形: | Taniguchi, Ayumu Kakuta, Yoichi Fujita, Kazutoshi Uemura, Motohide Kiuchi, Hiroshi Imamura, Ryoichi Miyagawa, Yasushi Nonomura, Norio Ueda, Yutaka |
キーワード: | Tuberous sclerosis Uterus Perivascular epithelioid cell tumor |
発行日: | 30-Nov-2019 |
出版者: | 泌尿器科紀要刊行会 |
誌名: | 泌尿器科紀要 |
巻: | 65 |
号: | 11 |
開始ページ: | 479 |
終了ページ: | 484 |
抄録: | We report a case of perivascular epithelioid cell tumor (PEComa) of the uterus associated with tuberous sclerosis complex discovered as a result of intraabdominal bleeding. A 54-year-old woman visited the department of obstetrics and gynecology with chief complaints of genital bleeding and abdominal pain lasting three weeks. Abdominal computed tomography (CT) revealed intraabdominal bleeding from the uterine corpus. She had a history of bilateral renal angiomyolipoma, which was treated with partial bilateral nephrectomy at age 25. Moreover, pulmonary lymphangioleiomyomatosis was diagnosed at age 43. Both conditions were detected by the CT scan during this hospitalization. Immediately after the CT scans, the patient entered a state of hemorrhagic shock, and we performed an emergency simple total hysterectomy. Histopathological examination on the resected specimen yielded a diagnosis of uterine perivascular epithelial cell tumor (PEComa). After making a definitive diagnosis of tuberous sclerosis complex (TSC), systemic evaluation was performed. As a result, multiple skin and intracranial lesions characteristic of TSC were identified and we stated administration of everolimus. |
著作権等: | 許諾条件により本文は2020/12/01に公開 |
DOI: | 10.14989/ActaUrolJap_65_11_479 |
URI: | http://hdl.handle.net/2433/245259 |
PubMed ID: | 31902183 |
出現コレクション: | Vol.65 No.11 |
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